Ankylosing Spondylitis

Last modified: 17 June 2022, 4:02:28 PM AEST
Origin / Etymology1 / 10
  • Ankylosing / Anklylosis
    • Fused bones
    • Ankylos = Greek = bent / crooked / curved
  • Spondylitis
    • Inflammation of vertebrae
  • Spondylosis
    • Any of various degenerative diseases of spine
    • Spondylos = Vertebrae
Definition / diagnostic criteria2 / 10
  • seronegative spondyloarthropathy
  • axial spondyloarthritis
  • multisystem inflammatory disease with extra-articular features
  • 0.1-0.8% prevalence
  • onset young adulthood
  • unknown cause
    • likely autoimmune mechanism
  • 85% patients have HLA-B27 antigen
    • HLA = Human Leucocyte Antigen
Complications / Issues3 / 10
  • A = Airway
    • TMJ dysfunction
  • A = C-spine
    • occult cervical fracture (with minimal trauma)
    • atlanto-axial subluxation
    • cervical fusion
  • B = Respiratory
    • Pulmonary fibrosis = parenchymal fibrosis = restrictive lung disease
    • Chest wall MSk disease
  • C = Cardiovascular
    • Aortic regurgitation
    • myocarditis
    • conduction defects
    • Cardiomegaly
    • Cardiomyopathy
    • Pericardial effusion
  • D = Neurological
    • Spondylolisthesis = causing cord compression
  • D = Ophthalmology
    • uveitis / iritis
      • common and maybe severe
  • E = Endocrine
  • F = Renal
    • Amyloid deposits
  • G = Gastrointestinal
  • H = Haematological
  • I = Immune
  • J = MSk
    • tendoachilles
    • costochondritis

Symptoms / History4 / 10
  • Back pain
    • radiating to sacro-iliac joints and hips
    • worse at night
    • improves after movement
Signs / Examination5 / 10
  • General inspection

    • stiff posture
    • kyphosis maybe present
  • Spinal tenderness

  • Sacroiliac joint tenderness

  • Hips = reduced ROM


Investigations6 / 10
  • RFTs
  • Echo
  • C-spine XR
  • Spine XR
    • bamboo spine = pathognomonic radiographic feature
      • ossification of outer fibres of annulus fibrosus of intervertebral discs
      • formation of marginal syndesmophytes
  • FBC
    • normochromic anaemia = AOCD
Management7 / 10
  • NSAIDs
  • Steroids
  • Immunomodulators
    • bone marrow suppression
    • Platelet dysfunction
    • Renal impairment
    • need for steroid coverage

Anaesthetic considerations8 / 10
  • Pre-op
    • consider multisystem disease features, esp cardiopulmonary
  • Intra-op
    • A = Minimise C-spine manipulation
      • consider AFOI
    • D = NA may be difficult / impossible
      • poor positioning
      • epidural space obliteration
      • ⬆risk epidural haematoma (ASRA)
      • paramedian approach + ultrasound ***
    • careful patient positioning = peripheral N injury
  • Post-op

Common questions / related topics9 / 10

Ank Spond + Pregnancy

  • Complicated due to difficult AW and NA
  • Have multiple plans in place

Ank Spond = Technique of intubation

  • Awake FOB
  • Asleep dual technique = VL + FOB + 2 operators

Ank Spond = Awake FOB failure

  • Defer surgery
  • Asleep FOB / awake trache

Ank Spond = Ruptured Achilles tendon

  • What problems do you anticipate?
  • Difficult positioning in prone position

Links / References10 / 10

https://en.wikipedia.org/wiki/Ankylosing_spondylitis

https://radiopaedia.org/articles/bamboo-spine-ankylosing-spondylitis